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The authors report 17 cases of symptomatic Chiari type II malformation occurring in two distinct age dependent population. In Group I, 13 neonates and infants in the first year of life presented with cranial nerve and brain stem dysfunction characterized by vocal cord paralysis, apnea, dysphagia and laryngeal stridor.
In Group II, 4 patients developed signs and symptoms after the first year of life. In this group, the presentation was more insidious and included neck pain and cerebellar manifestations. The surgical treatment consisted initially in shunt implantation or revision and when there was no improvement, posterior fossa decompression was performed. The response to the surgical treatment differed considerably between the two groups: older patients improved promptly after surgery and there was no casualties; in newborn and infants, especially those under 6 months of age, the mortality rate was The authors stress that prompt diagnosis and surgical intervention should be performed in order to produce a favorable outcome.
Os pacientes foram divididos em Grupos I idade inferior a 12 meses e Grupo II idade superior a 12 meses. Do total, 11 eram do sexo feminino e 6 do sexo masculino. Nos previamente derivados, a primeira medida foi certificar-se que o sistema funcionava adequadamente. Em todos os 3 houve ventriculite precedendo o quadro. Uma paciente encontra-se clinica e neurologicamente estabilizada, apesar de traqueostomizada. Cochrane et al.
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The dysraphic states: from syringomyelia to anencephaly. Amsterdam: Excerpta Medica, The cause of the Chiari malformation: a unified theory. Pediatr Neurosci ; Concepts Pediat Neurosurg ; Experience with surgical decompression of the Arnold-Chiari malformation in young infants with myelomeningocele. Venes JL. Multiple cranial nerve palsies in an infant with Arnold-Chiari malformation.
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Revisión bibliográfica sobre la sintomatología cognitiva en la malformación de Chiari tipo I
Arnold Chiari type I malformation with bilateral papilledema. ISSN Introduction: The Arnold Chiari malformation, or caudal cerebellar tonsilar ectopy, is a congenital defect of the posterior fossa, consisting in the descent of the cerebellar amygdalae 5mm below the foramen magnum. Clinically it presents as craneal hypertension headache, nystagmus, diplopia, VI craneal pair paralysis, tinnitus, dysphagia, weakness, paresthesia and spasticity.